Connective tissue nevi in Child
Synopsis

CTN may be isolated or occur as part of a syndrome, such as tuberous sclerosis (collagenomas known as shagreen patches and fibrous forehead plaque), familial cutaneous collagenomas, Proteus syndrome (cerebriform connective tissue nevus), and Buschke-Ollendorff syndrome (elastomas known as dermatofibrosis lenticularis disseminata). Acquired collagenoma (athlete's nodules) may occur at sites of sporting injuries, such as the feet, knuckles, or knees.
CTN have a variable clinical appearance. They may appear as skin-colored, light brown, or yellowish papules or plaques with a smooth, cobblestone, or peau d'orange surface.
Codes
D23.9 – Other benign neoplasm of skin, unspecified
SNOMEDCT:
400091006 – Connective tissue nevus of skin
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Last Updated:06/01/2021