Clinical manifestations are variable but include severe headaches, transient ischemic attacks or strokes, cranial neuropathies, seizures, and encephalopathy. In primary angiitis of the CNS, systemic symptoms such as fever, myalgias, rash, or weight loss are usually absent.
More recently, cerebral vasculitis also has been reported in children, but its incidence is unknown due to both its rarity as well as the possibility of it having gone undiagnosed. The signs and symptoms are the same.
I67.7 – Cerebral arteritis, not elsewhere classified
427020007 – Cerebral vasculitis
Differential Diagnosis & Pitfalls