Contents

SynopsisCodesLook ForDiagnostic PearlsDifferential Diagnosis & PitfallsBest TestsManagement PearlsTherapyReferences

View all Images (2)

Diastematomyelia in Child
Print
Other Resources UpToDate PubMed

Diastematomyelia in Child

Print Images (2)
Contributors: Bo Hoon Lee MD, Jamie Adams MD, Richard L. Barbano MD, PhD
Other Resources UpToDate PubMed

Alerts and Notices

Synopsis

Diastematomyelia : Low back pain, Neuropathy peripheral, Numbness, Paraplegia, Proximal muscle weakness, Urinary incontinence, Fecal incontinence, Paresthesias
Diastematomyelia, split-cord malformation (SCM), is a rare congenital abnormality in which there is partial or complete cleft in the spinal cord by a sagittal osseous or fibrous septum. It is seen predominantly in females, most often affecting the lower thoracic or upper lumbar segments. Clinically, diastematomyelia often presents as tethered cord syndrome (back pain, abnormal gait, spasticity, bowel / bladder incontinence) in children or young adults, although symptom onset may occur at any age. Patients may have a midline cutaneous abnormality such as a hairy patch or dimple over the affected area. There are two classifications:
  • SCM type 1 consists of two hemicords, each with its own dural sheath, separated by a bony or cartilaginous septum.
  • SCM type 2 consists of two hemicords within the same dural sheath but separated by a fibrous septum.

Codes

ICD10CM:
Q06.2 – Diastematomyelia

SNOMEDCT:
445308004 – Split spinal cord malformation

Look For

Subscription Required

Diagnostic Pearls

Subscription Required

Differential Diagnosis & Pitfalls

Best Tests

Subscription Required

Management Pearls

Subscription Required

Therapy

Subscription Required

References

Subscription Required

Last Reviewed:08/07/2018
Last Updated:01/13/2022
Copyright © 2023 VisualDx®. All rights reserved.
Diastematomyelia in Child
Print   View all Images (2)
(with subscription)
A medical illustration showing key findings of Diastematomyelia : Low back pain, Neuropathy peripheral, Numbness, Paraplegia, Proximal muscle weakness, Urinary incontinence, Fecal incontinence, Paresthesias
Imaging Studies image of Diastematomyelia - imageId=2381759. Click to open in gallery.
Copyright © 2023 VisualDx®. All rights reserved.