It is more common in patients with a heavy smoking history and may be accompanied by other signs of skin damage secondary to chronic sun exposure (for example, deep wrinkles). Other types of radiation exposure also increase the risk. Middle-aged men with Fitzpatrick skin types I and II are more commonly affected than women and individuals with darker skin colors. Because the disease is benign, any treatment other than sun protection measures is for cosmetic purposes only.
As this condition is acquired secondary to chronic sun exposure, it is not commonly seen in children or young adults, although cases have been reported in patients in their second decade of life.
L98.8 – Other specified disorders of the skin and subcutaneous tissue
111200005 – Favre-Racouchot syndrome
Differential Diagnosis & Pitfalls
- Colloid milia
- Acne vulgaris
- Sebaceous hyperplasia
- Other adnexal tumors such as trichoepitheliomas and apocrine hidrocystomas
- Squamous cell carcinoma
- In alkaptonuria, there may be blue or black pigmentation, but it does not present with the other signs of sun exposure seen in Favre-Racouchot syndrome.
- Cutis rhomboidalis nuchae