Poikilodermatous plaque-like hemangioma (PPLH) is an acquired vascular proliferation first described in 2019, and fewer than 20 cases have been reported to date. Clinically, PPLH presents as an asymptomatic, slow-growing, erythematous or violaceous atrophic plaque with variable scale. It is usually found on the lower extremities and most commonly presents as a single lesion; however, multiple lesions have been observed. The original series noted a strong male predominance. PPLH most commonly appears in the fifth decade or later.
The cause of PPLH is not known.
In the reported cases, lesions tended to persist and remained stable in size for up to 6 years.
Poikilodermatous plaque-like hemangioma
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Synopsis
Codes
ICD10CM:
D18.01 – Hemangioma of skin and subcutaneous tissue
SNOMEDCT:
271481007 – Hemangioma of skin and subcutaneous tissue
D18.01 – Hemangioma of skin and subcutaneous tissue
SNOMEDCT:
271481007 – Hemangioma of skin and subcutaneous tissue
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Differential Diagnosis & Pitfalls
- Poikilodermatous mycosis fungoides – Presents as multiple hypopigmented or hyperpigmented patches in younger patients on the trunk and flexural areas. This will show findings of cutaneous T-cell lymphoma on histology.
- Fixed drug eruption – Appears in the same location(s) every time the patient is exposed to a medication and resolves with discontinuation of the medication.
- Acrodermatitis chronica atrophicans – Presents as multiple lesions with a history of tick bite.
- Pigmented purpuric dermatoses – Present with irregular purpuric macules and plaques with pinpoint petechiae.
- Acquired elastotic hemangioma – Presents as a small, erythematous papule on sun-exposed areas of the upper extremities.
- Insect bite reaction
- Acroangiodermatitis
- Kaposi sarcoma
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Last Reviewed:05/12/2021
Last Updated:05/12/2021
Last Updated:05/12/2021