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Pseudoainhum in Adult
Other Resources UpToDate PubMed

Pseudoainhum in Adult

Contributors: Siddhanth Hegde, Benjamin L. Mazer MD, MBA, Susan Burgin MD
Other Resources UpToDate PubMed

Synopsis

Pseudoainhum is a very rare condition in which a constriction band forms around a digit or extremity. Unlike ainhum, in which digital constriction bands develop spontaneously, pseudoainhum occurs in the setting of an underlying cutaneous condition or initiating factor.

Amniotic bands may cause congenital pseudoainhum. Acquired pseudoainhum can occur after external trauma from a hair or thread wrapped around a digit, or in association with an inherited palmoplantar keratoderma, such as Vohwinkel syndrome, Olmsted syndrome, Mal de Meleda, loricrin keratoderma, Papillon-Lefèvre syndrome, and KLICK syndrome (keratosis linearis with ichthyosis congenita and sclerosing keratoderma). Additionally, pseudoainhum has rarely been reported to coexist with psoriasis and lamellar ichthyosis.

Pseudoainhum typically affects the digits. It can present in one of 4 stages: an asymptomatic groove of constricting soft tissue (stage 1); ulceration of the floor of the groove (stage 2); bony erosion (stage 3); and spontaneous autoamputation (stage 4). The disease typically progresses between stages slowly over months to years, but a more rapid progression over days has been reported.

Codes

ICD10CM:
L94.9 – Ainhum

SNOMEDCT:
19988008 – Pseudoainhum

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Diagnostic Pearls

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Differential Diagnosis & Pitfalls

Ainhum:
  • Idiopathic disease that leads to formation and progression of constriction bands on the extremities, which can lead to autoamputation.
  • Ainhum can only be diagnosed in the absence of another underlying condition.
Autoamputation unrelated to pseudoainhum:

Best Tests

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Management Pearls

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Therapy

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References

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Last Reviewed:09/02/2021
Last Updated:09/08/2021
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Pseudoainhum in Adult
A medical illustration showing key findings of Pseudoainhum : Toe pain, Autoamputation
Clinical image of Pseudoainhum - imageId=7139648. Click to open in gallery.  caption: 'Crusted constriction bands on the toes.'
Crusted constriction bands on the toes.
Copyright © 2022 VisualDx®. All rights reserved.