Pseudoporphyria - External and Internal Eye
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Synopsis
While commonly associated with NSAIDs, antibiotics, and diuretics with sulfa moieties, pseudoporphyria can also be seen in chronic renal failure (with or without hemodialysis) and with ultraviolet A (UVA) exposure such as tanning beds, psoralen plus UVA (PUVA) therapy, and excessive natural sun.
Blue-gray eye color has been reported as a risk factor for pseudoporphyria due to NSAIDS in children.
Codes
E80.20 – Unspecified porphyria
SNOMEDCT:
95565000 – Pseudoporphyria
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Last Updated:12/26/2018