Retroperitoneal cystic lymphangioma
Alerts and Notices
Synopsis
These tumors can be asymptomatic, but often, due to their size and location, patients will present with a palpable abdominal mass, bowel obstruction, abdominal pain, anorexia, weight loss, ascites, or obstructive nephropathy from ureter compression. Asymptomatic cases can be found incidentally during surgery or autopsy.
The diagnosis of a cystic lymphangioma typically requires pathology, as the appearance of a complex cyst on cross-sectional imaging is not specific to these types of tumors.
Codes
ICD10CM:D18.1 – Lymphangioma, any site
SNOMEDCT:
40225001 – Cystic lymphangioma
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Diagnostic Pearls
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Differential Diagnosis & Pitfalls
Cystic tumor, retroperitoneum:- Cystic mesothelioma
- Teratoma
- Sarcoma
- Metastases (gastric or ovarian primary malignancy)
- Malignant mesenchymoma
- Urothelial or foregut complex or simple cysts
- Microcystic pancreatic adenoma
- Retroperitoneal hematoma
- Duplication cyst
- Ovarian cyst
- Pancreatic pseudocyst
- Müllerian cyst
- Epidermoid cyst
- Tailgut cyst
- Paraganglioma
- Neuroblastoma
- Retroperitoneal pseudomyxoma
- Lymphocele
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Therapy
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References
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Last Reviewed:03/06/2018
Last Updated:04/12/2018
Last Updated:04/12/2018