Congenital smooth muscle hamartomas develop during fetal life and are characterized by localized proliferations of smooth muscle bundles in the dermis with overlying vellus hairs. Congenital smooth muscle hamartomas may be noticed at birth or during early infancy. There are no systemic symptoms. The estimated prevalence is 1 in 2600 births with a slight male predominance.
Smooth muscle hamartomas are benign and, thus, the prognosis is excellent. Pigmentation and hair tend to become less noticeable with age.
Smooth muscle hamartoma in Infant/Neonate
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Synopsis
Codes
ICD10CM:
Q85.9 – Phakomatosis, unspecified
SNOMEDCT:
239145008 – Diffuse smooth muscle hamartoma
Q85.9 – Phakomatosis, unspecified
SNOMEDCT:
239145008 – Diffuse smooth muscle hamartoma
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Last Updated:10/01/2018
Smooth muscle hamartoma in Infant/Neonate