Infantile fibrosarcoma
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Synopsis

Infantile fibrosarcomas have a better prognosis than the adult form, with a 5-year survival rate of 84% seen in one study.
Codes
ICD10CM:C49.9 – Malignant neoplasm of connective and soft tissue, unspecified
SNOMEDCT:
403996004 – Infantile fibrosarcoma
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Diagnostic Pearls
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Differential Diagnosis & Pitfalls
- Infantile hemangioma – May be confused with an infantile fibrosarcoma because of the possible presence of superficial ectatic veins in fibrosarcomas.
- Infantile myofibromatosis
- Rhabdomyosarcoma
- Neuroblastoma
- Primitive neuroectodermal tumor
Best Tests
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Management Pearls
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Therapy
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References
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Last Reviewed:07/06/2021
Last Updated:07/22/2021
Last Updated:07/22/2021